{"id":3221,"date":"2026-09-04T12:07:19","date_gmt":"2026-09-04T09:07:19","guid":{"rendered":"https:\/\/pediatria-spisanie.eu\/2026\/09\/04\/von-willebrand-disease-in-paediatric-ent-practice-a-case-series-and-practical-recommendations\/"},"modified":"2026-09-04T17:17:21","modified_gmt":"2026-09-04T14:17:21","slug":"von-willebrand-disease-in-paediatric-ent-practice-a-case-series-and-practical-recommendations","status":"publish","type":"post","link":"https:\/\/pediatria-spisanie.eu\/en\/2026\/09\/04\/von-willebrand-disease-in-paediatric-ent-practice-a-case-series-and-practical-recommendations\/","title":{"rendered":"Von Willebrand disease in paediatric ENT practice \u2013 a case series and practical recommendations"},"content":{"rendered":"\n

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\nI. Stancheva<\/strong>\n<\/p>\n\n

\nDepartment of ENT Diseases, Medical University \u2013 Sofia
\nUMBHAL \u201cTsaritsa Ioanna \u2013 ISUL\u201d, Sofia\n<\/p>\n\n\t\t<\/div>\n\t<\/div>\n\t\n\t\n\n

<\/div>\n\n\n\n

Abstract<\/h2>\n\n\n\n

Von Willebrand disease (VWD) is the most common inherited bleeding disorder that often remains unrecognised in childhood. One of its leading manifestations is recurrent epistaxis.<\/p>\n\n\n\n

Aim.<\/strong> To present a series of paediatric cases with initial presentation in ear\u2013nose\u2013throat (ENT) practice and to propose a short focused-history questionnaire.<\/p>\n\n\n\n

Material and methods.<\/strong> A retrospective series of three clinical cases: a boy with recurrent epistaxis; a family with two brothers, diagnosed preoperatively and following recurrent epistaxis, respectively; and a 3-year-old girl with severe bleeding after adenoidectomy.<\/p>\n\n\n\n

Results.<\/strong> In all three cases the routine coagulation parameters proved insufficient \u2013 a focused bleeding and family history was decisive. Conclusion.<\/strong> The history often outperforms routine coagulation screening in selecting patients for specific testing, in line with current international recommendations. We propose a short questionnaire and stress the need for clinician training and patient awareness.<\/p>\n\n\n\n

Keywords:<\/strong><\/strong> von Willebrand disease, epistaxis, children, haemostasis, focused history<\/em><\/em><\/em><\/p>\n\n\n

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Bibliography<\/strong><\/h2>\n\n\n\n
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    Address for correspondence:<\/strong><\/p>\n\n\n\n

    Iglika Stancheva <\/p>\n\n\n\n

    Department of Otorhinolaryngology, Faculty of Medicine, Medical University of Sofia,
    University Hospital \u201cTsaritsa Yoanna – ISUL\u201d, Sofia <\/p>\n\n\n\n

    8, \u201cBialo more\u201d, Str.<\/p>\n\n\n\n

    e-mail: iglika_stancheva@yahoo.com<\/a><\/p>\n\n\n\n

    <\/p>\n\n\n\n

    <\/p>\n\n\n\n

    <\/p>\n","protected":false},"excerpt":{"rendered":"

    I. Stancheva ||| Department of ENT Diseases, Medical University \u2013 Sofia ||| UMBHAL \u201cTsaritsa Ioanna \u2013 ISUL\u201d, Sofia<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_pediatria_doi":"10.66223\/pediatria.2026.3.007","footnotes":""},"categories":[1301,2684,2679,3399,1],"tags":[239,3377,3424,3374,3375,3426,3376,3404,3368,3370,3369,42,3372,3373,3371],"class_list":["post-3221","post","type-post","status-publish","format-standard","hentry","category-articles","category-issue-3-2026","category-broj-3-2026","category-statii","tag-children","tag-epistaxis","tag-focused-history","tag-haemostasis","tag-von-willebrand-disease","tag-von-willebrand-disease-in-paediatric-ent-practice-a-case-series-and-practical-recommendations","tag-bolest-na-fon-vilebrand","tag-bolestta-na-fon-vilebrand-v-detskata-otorinolaringologichna-praktika-seriya-ot-klinichni-sluchai-i-prakticheski-preporaki","tag-decza","tag-epistaksis","tag-nasochena-anamneza","tag-hemostaza"],"_links":{"self":[{"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/posts\/3221","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/comments?post=3221"}],"version-history":[{"count":4,"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/posts\/3221\/revisions"}],"predecessor-version":[{"id":3232,"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/posts\/3221\/revisions\/3232"}],"wp:attachment":[{"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/media?parent=3221"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/categories?post=3221"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/pediatria-spisanie.eu\/en\/wp-json\/wp\/v2\/tags?post=3221"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}